Hypohydrotic ectodermal dysplasia is a common group of hereditary diseases, with congenital tooth loss as the predominant oral symptom. The prosthodontics of hypohydrotic ectodermal dysplasia is special because most
of the affected patients are pre- adolescents, whose jaw bones and alveolar process are lack of development. A sequence treatment option is applied in the treatment procedure. This review included the clinical features and
prosthodontics of hypohydrotic ectodermal dysplasia, depending on large numbers of relavant literatures.